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Are you packing your meals with protein, thinking more is always better? You’re not alone. Protein is a vital nutrient known ...
The new infusion for maple syrup urine disease is for patients who cannot have an oral or enteral branched-chain amino ...
Protein is arguably the most popular nutrient among Western consumers. Can you have too much of it, and if so, what are the ...
The median leucine level at diagnosis was 1,693 µmol/L (IQR 965-2,836 ... Please cite this article as: Herber S, Schwartz IV, Nalin T, Netto CB, Junior JS, Santos ML, et al. Maple syrup urine disease ...
Urine colour can provide important diagnostic information. For example, orange urine may indicate a urinary tract infection (UTI), liver disease, or bile duct disorder. Dr Marco Franzoi and ...
Maple syrup urine disease (MSUD ... the mitochondrial BCKDH complex that decarboxylates ketoacid derivatives of leucine, isoleucine, and valine. MSUD can be treated by a strictly controlled ...
Leucine, in particular ... Proper hydration can help dilute urine, reducing the risk of urinary tract infections (UTIs) and other bladder-related issues that are common among older adults.
Urine color changes in early pregnancy When ... that prevents your body from properly breaking down three amino acids: leucine, isoleucine, and valine. When these amino acids build up in your ...
Valine is one of three branched-chain amino acids (BCAA), compounds the body requires to create and maintain proteins, brain chemicals, and hormones. The body can't make its own, so foods that contain ...
“Maple Syrup Urine Disease (MSUD) is a neonatal condition caused by an enzyme deficiency within the cells, which hinders the metabolism of branched-chain amino acids, specifically ...
In this rare inherited genetic metabolic disorder, the body cannot process certain amino acids, especially leucine, causing a harmful build-up of substances in the blood and urine. Amino acids are ...